Product overview:

Anti-HIBCH mouse monoclonal antibody, clone LBI3F6

Field of research:

beta-Alanine metabolism, Metabolic pathways, Propanoate metabolism, Valine, leucine and isoleucine degradation

Summary:

This gene encodes the enzyme responsible for hydrolysis of both HIBYL-CoA and beta-hydroxypropionyl-CoA. Mutations in this gene have been associated with 3-hyroxyisobutyryl-CoA hydrolase deficiency. Alternative splicing results in multiple transcript variants.

Alternative names:

HIBYLCOAH

Species reactivity:

Human

Host:

Mouse

Target:

HIBCH

Isotype:

IgG1

Immunogen:

Full length human recombinant protein of human HIBCH (NP_055177) produced in HEK293T cell.

Clone:

LBI3F6

Conjugation:

Unconjugated

Gene name:

3-hydroxyisobutyryl-CoA hydrolase

Symbol:

HIBCH

Pathway:

beta-Alanine metabolism, Metabolic pathways, Propanoate metabolism, Valine, leucine and isoleucine degradation

Function:

Request info at info@sobekbio.com

Purification:

Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G)

Concentration:

0.61 mg/ml

Form:

PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Applications & dilution:

WB 1:2000, IF 1:100, FLOW 1:100

Storage buffer:

PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Storage:

Store at +4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.

More info:

Email: info@sobekbio.com

Orders:

Email: orders@sobekbio.com