Background:

cofactor:Binds 2 heme groups non-covalently.|disease:Defects in MT-CYB are a rare cause of mitochondrial dysfunction underlying different myopathies. They include mitochondrial encephalomyopathy| hypertrophic cardiomyopathy (HCM)| and sporadic mitochondrial myopathy (MM). In mitochondrial myopathy| exercise intolerance is the predominant symptom. Additional features include lactic acidosis| muscle weakness and/or myoglobinuria. Defects in MTCYB are also found in cases of exercise intolerance accompanied by deafness| mental retardation| retinitis pigmentosa| cataract| growth retardation| epilepsy (multisystem disorder).|disease:Defects in MT-CYB are the cause of cardiomyopathy infantile histiocytoid (CMIH)

Classification:

Primary antibody

Alternative names:

Cytochrome b; Cytochrome b; Complex III subunit 3; Complex III subunit III; Cytochrome b-c1 complex subunit 3; Ubiquinol-cytochrome-c reductase complex cytochrome b subunit

Species reactivity:

Human, Mouse

Host:

Rabbit

Isotype:

IgG

Immunogen:

Synthesized peptide derived from human Cytochrome b. at AA range: 331-380

Concentration:

1 mg/ml

Molecular weight:

Applications:

WB, ELISA

Storage:

-20°C for 1 year

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